Amino acid metabolism (WP662)
Mus musculus
A complete overview of the metabolism of all 20 amino acids
Authors
Martijn Van Iersel , Martina Summer-Kutmon , Egon Willighagen , and Eric WeitzActivity
Discuss this pathway
Check for ongoing discussions or start your own.
Cited In
- Bioenergetic defects in muscle fibers of RYR1 mutant knock-in mice associated with malignant hyperthermia (2020).
- Proteomic profiling of salivary gland after nonviral gene transfer mediated by conventional plasmids and minicircles (2014).
- Podocyte-specific KLF6 primes proximal tubule CaMK1D signaling to attenuate diabetic kidney disease (2024).
- Isoschaftoside in Fig Leaf Tea Alleviates Nonalcoholic Fatty Liver Disease in Mice via the Regulation of Macrophage Polarity (2025).
Are you planning to include this pathway in your next publication? See How to Cite and add a link here to your paper once it's online.
Organisms
Mus musculusCommunities
Annotations
Pathway Ontology
amino acid metabolic pathway amino acid metabolic pathway amino acid metabolic pathway amino acid metabolic pathwayLabel | Type | Compact URI | Comment |
---|---|---|---|
Ethanol | Metabolite | hmdb:HMDB0000108 | |
Methionine | Metabolite | hmdb:HMDB0000696 | |
Indoleacetate | Metabolite | hmdb:HMDB0000197 | |
Aconitate | Metabolite | hmdb:HMDB0000072 | |
Oxaloacetate | Metabolite | hmdb:HMDB0000223 | |
Aspartate | Metabolite | hmdb:HMDB0000191 | |
Leucine | Metabolite | hmdb:HMDB0000687 | |
Urea | Metabolite | hmdb:HMDB0000294 | |
Fumarate | Metabolite | hmdb:HMDB0000134 | |
isocitrate | Metabolite | hmdb:HMDB0000193 | |
Citrate | Metabolite | hmdb:HMDB0000094 | |
methylhistamine | Metabolite | hmdb:HMDB0000898 | |
Dopamine | Metabolite | hmdb:HMDB0000073 | |
Cystathionine | Metabolite | hmdb:HMDB0000099 | |
Carbamoyl-aspartate | Metabolite | hmdb:HMDB0000828 | |
Histidine | Metabolite | hmdb:HMDB0000177 | |
Pyruvate | Metabolite | hmdb:HMDB0000243 | |
5-OH-Trp | Metabolite | hmdb:HMDB0000472 | |
B-OH-butyrate | Metabolite | hmdb:HMDB0000011 | |
Glutamine | Metabolite | hmdb:HMDB0000641 | |
Glucose | Metabolite | hmdb:HMDB0000122 | |
Creatine P | Metabolite | hmdb:HMDB0001511 | |
Threonine | Metabolite | hmdb:HMDB0000167 | |
Glycine | Metabolite | hmdb:HMDB0000123 | |
Isoleucine | Metabolite | hmdb:HMDB0000172 | |
Arginine | Metabolite | hmdb:HMDB0000517 | |
Histamine | Metabolite | hmdb:HMDB0000870 | |
Melanin | Metabolite | hmdb:HMDB0004068 | |
Tyrosine | Metabolite | hmdb:HMDB0000158 | |
Ornithine | Metabolite | hmdb:HMDB0000214 | |
hydroxy-proline | Metabolite | hmdb:HMDB0000725 | |
mercaptopyruvate | Metabolite | hmdb:HMDB0001368 | |
Alanine | Metabolite | hmdb:HMDB0000161 | |
Asparagine | Metabolite | hmdb:HMDB0000168 | |
Homocysteine | Metabolite | hmdb:HMDB0000742 | |
Tryptamine | Metabolite | hmdb:HMDB0000303 | |
carbamoyl-P | Metabolite | hmdb:HMDB0001096 | |
Succinyl-CoA | Metabolite | hmdb:HMDB0001022 | |
Citrulline | Metabolite | hmdb:HMDB0000904 | |
Cysteine | Metabolite | hmdb:HMDB0000574 | |
Thyroxine | Metabolite | hmdb:HMDB0000248 | |
Spermidine | Metabolite | hmdb:HMDB0001257 | |
oxo-isocaproate | Metabolite | chebi:17865 | |
Serine | Metabolite | hmdb:HMDB0000187 | |
Spermine | Metabolite | hmdb:HMDB0001256 | |
Tryptophan | Metabolite | hmdb:HMDB0000929 | |
Oxobutyrate | Metabolite | hmdb:HMDB0000005 | |
P-enolpyruvate | Metabolite | hmdb:HMDB0000263 | |
Guanidinoacetate P | Metabolite | hmdb:HMDB0003705 | |
Lactate | Metabolite | hmdb:HMDB0000190 | |
OH-indoleacetate | Metabolite | hmdb:HMDB0000763 | |
methylmalonyl-CoA | Metabolite | chebi:15465 | |
Guanidinoacetate | Metabolite | hmdb:HMDB0000128 | |
Succinate | Metabolite | hmdb:HMDB0000254 | |
valine | Metabolite | hmdb:HMDB0000883 | |
Phenylalanine | Metabolite | hmdb:HMDB0000159 | |
oxo-methyl-valerate | Metabolite | chebi:35146 | |
oxo-isovalerate | Metabolite | chebi:11851 | |
Putrescine | Metabolite | hmdb:HMDB0001414 | |
methylmalonate semialdehyde | Metabolite | chebi:16256 | |
Serotonin | Metabolite | hmdb:HMDB0000259 | |
Dihydro-orotate | Metabolite | hmdb:HMDB0003349 | |
Glutamate | Metabolite | hmdb:HMDB0000148 | |
Malate | Metabolite | hmdb:HMDB0000156 | |
Proline | Metabolite | hmdb:HMDB0000162 | |
Indoleacetaldehyde | Metabolite | hmdb:HMDB0001190 | |
HCO3 | Metabolite | hmdb:HMDB0003538 | |
NADP | Metabolite | hmdb:HMDB0000217 | |
Met-tRNA | Metabolite | chebi:16635 | |
Arginino-succinate | Metabolite | hmdb:HMDB0000052 | |
N-Formylkynurenine | Metabolite | hmdb:HMDB0001200 | |
Arg-tRNA | Metabolite | chebi:18366 | |
Ala-tRNA | Metabolite | chebi:17732 | |
Trp-tRNA | Metabolite | chebi:29159 | |
isobutyryl-CoA | Metabolite | chebi:15479 | |
Val-tRNA | Metabolite | chebi:29164 | |
Leu-tRNA | Metabolite | chebi:16624 | |
Ile-tRNA | Metabolite | chebi:29160 | |
Isovaleryl-CoA | Metabolite | hmdb:HMDB0001113 | |
Methylbutyryl-CoA | Metabolite | hmdb:HMDB0001041 | |
Acetyl-CoA | Metabolite | hmdb:HMDB0001206 | |
OH-methylglutaryl-CoA | Metabolite | hmdb:HMDB0001375 | |
methacrylyl-CoA | Metabolite | chebi:27754 | |
OH-isobutyrate | Metabolite | chebi:19641 | |
Tiglyl-CoA | Metabolite | hmdb:HMDB0002054 | |
OH-isovaleryl-CoA | Metabolite | hmdb:HMDB0006870 | |
Methylacetoacetyl-CoA | Metabolite | chebi:15476 | |
OH-isobutyryl-CoA | Metabolite | hmdb:HMDB0001052 | |
Methylcrotonyl-CoA | Metabolite | hmdb:HMDB0001493 | |
Methyl-OH-butyryl-CoA | Metabolite | hmdb:HMDB0001356 | |
Propionyl-CoA | Metabolite | hmdb:HMDB0001275 | |
Methylglutaconyl-CoA | Metabolite | hmdb:HMDB0001057 | |
His-tRNA | Metabolite | chebi:29155 | |
pyrroline carboxylate | Metabolite | hmdb:HMDB0006875 | |
Glu-tRNA | Metabolite | chebi:29157 | |
glutamate semialdehyde | Metabolite | chebi:15757 | |
glutamyl-P | Metabolite | chebi:21314 | |
Imidazole acetaldehyde | Metabolite | hmdb:HMDB0003905 | |
2-oxo-glutarate | Metabolite | chebi:16810 | |
glutamyl-cysteine | Metabolite | chebi:17515 | |
Red. Glutathione | Metabolite | hmdb:HMDB0000125 | |
R-S-glutathione | Metabolite | chebi:17021 | |
Ox. glutathione | Metabolite | hmdb:HMDB0003337 | |
Phe-tRNA | Metabolite | chebi:29153 | |
homogentisate | Metabolite | chebi:16169 | |
Epinephrine | Metabolite | hmdb:HMDB0000068 | |
Norepinephrine | Metabolite | hmdb:HMDB0000216 | |
Tyr-tRNA | Metabolite | chebi:29161 | |
Gsr | GeneProduct | mgi:MGI:95804 | |
Hdc | GeneProduct | mgi:MGI:96062 | |
Cbs | GeneProduct | mgi:MGI:88285 | |
Sms | GeneProduct | mgi:MGI:109490 | |
Mdh1 | GeneProduct | mgi:MGI:97051 | |
Gst | GeneProduct | mgi:MGI:1309515 | |
Pkm2 | GeneProduct | mgi:MGI:97591 | |
Ass1 | GeneProduct | mgi:MGI:88090 | |
Aoc3 | GeneProduct | mgi:MGI:1306797 | |
Eprs | GeneProduct | mgi:MGI:97838 | |
Dld | GeneProduct | mgi:MGI:107450 | |
Pck1 | GeneProduct | mgi:MGI:97501 | |
Glud | GeneProduct | mgi:MGI:95753 | |
Hmgcs2 | GeneProduct | mgi:MGI:101939 | |
Hnmt | GeneProduct | mgi:MGI:2153181 | |
Ddc | GeneProduct | mgi:MGI:94876 | |
Acadm | GeneProduct | mgi:MGI:87867 | |
Got2 | GeneProduct | mgi:MGI:95792 | |
Auh | GeneProduct | mgi:MGI:1338011 | |
Pdk4 | GeneProduct | mgi:MGI:1351481 | |
Prodh | GeneProduct | ncbigene:19125 | |
Dlst | GeneProduct | mgi:MGI:1926170 | |
Fah | GeneProduct | mgi:MGI:95482 | |
Ehhadh | GeneProduct | mgi:MGI:1277964 | |
Hal | GeneProduct | mgi:MGI:96010 | |
Iars | GeneProduct | mgi:MGI:2145219 | |
Aldh1a1 | GeneProduct | mgi:MGI:1353450 | |
Hibch | GeneProduct | mgi:MGI:1923792 | |
Tat | GeneProduct | mgi:MGI:98487 | |
Cad | GeneProduct | mgi:MGI:1916969 | |
Mars2 | GeneProduct | mgi:MGI:2444136 | |
Bhmt | GeneProduct | mgi:MGI:1339972 | |
Bcat1 | GeneProduct | mgi:MGI:104861 | |
Acaa1 | GeneProduct | mgi:MGI:2148491 | |
Hibadh | GeneProduct | mgi:MGI:1889802 | |
Gpt | GeneProduct | mgi:MGI:1915391 | |
P4ha2 | GeneProduct | mgi:MGI:894286 | |
Pdha1 | GeneProduct | ncbigene:18597 | |
Tpo | GeneProduct | mgi:MGI:98813 | |
Gclc | GeneProduct | mgi:MGI:104995 | |
Adh5 | GeneProduct | mgi:MGI:87929 | |
Oat | GeneProduct | mgi:MGI:97394 | |
pdhp | GeneProduct | ncbigene:242083 | |
Adh4 | GeneProduct | mgi:MGI:1349472 | |
Maoa | GeneProduct | mgi:MGI:96915 | |
Th | GeneProduct | mgi:MGI:98735 | |
Sds | GeneProduct | mgi:MGI:98270 | |
Lars2 | GeneProduct | mgi:MGI:2142973 | |
G6Pase | GeneProduct | ncbigene:14378 | |
Wars | GeneProduct | mgi:MGI:104630 | |
Ldh1 | GeneProduct | mgi:MGI:96759 | |
Adh1 | GeneProduct | mgi:MGI:87921 | |
Gls | GeneProduct | mgi:MGI:95752 | |
Sdha | GeneProduct | mgi:MGI:1914195 | |
phtRNAs | GeneProduct | mgi:MGI:1346035 | |
Asns | GeneProduct | mgi:MGI:1350929 | |
Pdha1 ina | GeneProduct | ncbigene:18597 | |
Aldh7a1 | GeneProduct | mgi:MGI:108186 | |
Mpst | GeneProduct | mgi:MGI:2179733 | |
Suclg1 | GeneProduct | mgi:MGI:1927234 | |
Hmgcl | GeneProduct | mgi:MGI:96158 | |
Adh7 | GeneProduct | mgi:MGI:87926 | |
Pcx | GeneProduct | mgi:MGI:97520 | |
Pycr1 | GeneProduct | mgi:MGI:2384795 | |
Ogdh | GeneProduct | ncbigene:18293 | |
Asl | GeneProduct | mgi:MGI:88084 | |
Gss | GeneProduct | mgi:MGI:95852 | |
Fh1 | GeneProduct | ncbigene:14194 | |
Cth | GeneProduct | mgi:MGI:1339968 | |
Tph1 | GeneProduct | mgi:MGI:98796 | |
Mut | GeneProduct | mgi:MGI:97239 | |
Arg1 | GeneProduct | mgi:MGI:88070 | |
Mdh2 | GeneProduct | mgi:MGI:97050 | |
Idh1 | GeneProduct | mgi:MGI:96413 | |
Pnmt | GeneProduct | mgi:MGI:97724 | |
Dbh | GeneProduct | mgi:MGI:94864 | |
Aco2 | GeneProduct | mgi:MGI:87880 | |
Glns | GeneProduct | mgi:MGI:95739 | |
Rars | GeneProduct | mgi:MGI:1914297 | |
Mccc1 | GeneProduct | mgi:MGI:1919289 | |
Odc | GeneProduct | mgi:MGI:97402 | |
Gftcd | GeneProduct | mgi:MGI:1339962 | |
Pycs | GeneProduct | mgi:MGI:1888908 | |
Got1 | GeneProduct | mgi:MGI:95791 | |
Cs | GeneProduct | mgi:MGI:88529 | |
Acly | GeneProduct | mgi:MGI:103251 | |
Vars2 | GeneProduct | mgi:MGI:90675 | |
Pdhx | GeneProduct | mgi:MGI:1351627 | |
Tdo2 | GeneProduct | mgi:MGI:1928486 | |
Otc | GeneProduct | mgi:MGI:97448 | |
Sdhd | GeneProduct | mgi:MGI:1914175 | |
Acas2l | GeneProduct | mgi:MGI:1915988 | |
CPS | GeneProduct | mgi:MGI:891996 | |
Srm | GeneProduct | mgi:MGI:102690 | |
Hadhsc | GeneProduct | mgi:MGI:96009 | |
Arg2 | GeneProduct | mgi:MGI:1330806 |